FGF-2 Polyclonal Antibody
¥680.00
- 产品信息
商品描述
靶点-Target
SGSH
反应性
Human
应用
WB,IHC,IF,ICC
宿主物种-Host Species
Rabbit
同种型-Isotype
IgG,Kappa
偶联-Conjugate
Unmodified
MW(Observed)
55kD
推荐稀释比
WB 1:1000-5000;IHC 1:100-300;ICC/IF 1:100-300
组成
PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA
纯化工艺
Protein A
储存
-15°C to -25°C/1 year(Do not lower than -25°C)
克隆性
Monoclonal
克隆号
PT0814R
特异性
Endogenous
基因名称
SGSH;HSS
蛋白名称
N-sulphoglucosamine sulphohydrolase;Sulfoglucosamine sulfamidase;Sulphamidase;
别名
SGSH;HSS;N-sulphoglucosamine sulphohydrolase ;Sulfoglucosamine sulfamidase;Sulphamidase;
Organism-1
Human
基因ID-1
6448
SwissProt-1
P51688
背景
This gene encodes the enzyme sulfamidase; one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
细胞定位
Lysosome.
