- 产品信息
商品描述
靶点-Target
CLN6
反应性
Human
应用
WB,IHC,IF,ELISA
宿主物种-Host Species
Rabbit
同种型-Isotype
IgG
修饰-Modification
Unmodified
MW(Observed)
40kD
推荐稀释比
WB 1:500-1:2000;IHC 1:100-1:300;ELISA 1:40000;IF 1:50-200
组成
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
纯化工艺
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
储存
-15°C to -25°C/1 year(Do not lower than -25°C)
浓度
1 mg/ml
克隆性
Polyclonal
免疫原
The antiserum was produced against synthesized peptide derived from human CLN6. AA range:221-270
特异性
CLN6 Polyclonal Antibody detects endogenous levels of CLN6 protein.
基因名称
CLN6
蛋白名称
Ceroid-lipofuscinosis neuronal protein 6
别名
CLN6;Ceroid-lipofuscinosis neuronal protein 6;Protein CLN6
Organism-1
Human
基因ID-1
54982
SwissProt-1
Q9NWW5
背景
This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008],
细胞定位
Endoplasmic reticulum membrane ; Multi-pass membrane protein . Endoplasmic reticulum .





