- 产品信息
商品描述
靶点-Target
CLN1
反应性
Human,Mouse,Rat
应用
IHC,IF,ELISA
宿主物种-Host Species
Rabbit
同种型-Isotype
IgG
修饰-Modification
Unmodified
MW(Observed)
37kD
推荐稀释比
IHC 1:100-1:300;ELISA 1:10000;IF 1:50-200
组成
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
纯化工艺
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
储存
-15°C to -25°C/1 year(Do not lower than -25°C)
浓度
1 mg/ml
克隆性
Polyclonal
免疫原
The antiserum was produced against synthesized peptide derived from human CLN1. AA range:16-65
特异性
CLN1 Polyclonal Antibody detects endogenous levels of CLN1 protein.
基因名称
PPT1
蛋白名称
Palmitoyl-protein thioesterase 1
别名
PPT1;PPT;Palmitoyl-protein thioesterase 1;PPT-1;Palmitoyl-protein hydrolase 1
Organism-1
Human
基因ID-1
5538
SwissProt-1
P50897
Organism-2
Mouse
基因ID-2
19063
SwissProt-2
O88531
Organism-3
Rat
基因ID-3
29411
SwissProt-3
P45479
背景
The protein encoded by this gene is a small glycoprotein involved in the catabolism of lipid-modified proteins during lysosomal degradation. The encoded enzyme removes thioester-linked fatty acyl groups such as palmitate from cysteine residues. Defects in this gene are a cause of infantile neuronal ceroid lipofuscinosis 1 (CLN1, or INCL) and neuronal ceroid lipofuscinosis 4 (CLN4). Two transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, Dec 2008],
细胞定位
Lysosome . Secreted .





