FGF-2 Polyclonal Antibody
¥680.00
- 产品信息
商品描述
靶点-Target
LYAG
反应性
Human,Mouse,Rat
应用
WB
宿主物种-Host Species
Rabbit
同种型-Isotype
IgG
修饰-Modification
Unmodified
MW(Observed)
105kD
推荐稀释比
WB 1:500-2000
组成
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
纯化工艺
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
储存
-15°C to -25°C/1 year(Do not lower than -25°C)
浓度
1 mg/ml
克隆性
Polyclonal
免疫原
Synthesized peptide derived from human LYAG AA range: 432-482
特异性
This antibody detects endogenous levels of LYAG at Human/Mouse/Rat
基因名称
GAA
蛋白名称
LYAG
别名
Lysosomal alpha-glucosidase;Acid maltase;Aglucosidase alfa;[Cleaved into: 76 kDa lysosomal alpha-glucosidase;70 kDa lysosomal alpha-glucosidase]
Organism-1
Human
基因ID-1
2548
SwissProt-1
P10253
Organism-2
Mouse
基因ID-2
14387
SwissProt-2
P70699
Organism-3
Rat
基因ID-3
367562
SwissProt-3
Q6P7A9
背景
This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2016],
细胞定位
Lysosome . Lysosome membrane .
